Granulomatosis with polyangiitis (CNS manifestations)

CNS manifestations of granulomatosis with polyangiitis (GPA) (previously known as Wegener granulomatosis) are rare. Granulomatosis with polyangiitis is a multi-system systemic necrotizing non-caseating granulomatous vasculitis affecting small to medium-sized arteries, capillaries and veins.


CNS manifestations of GPA occur only in ~5% (range 2-9%) of the patients 1,2.


GPA manifests in the CNS as 1,2:

Article information

rID: 40104
Synonyms or Alternate Spellings:
  • Granulomatosis with polyangiitis - CNS manifestations
  • Wegner granulomatosis: CNS manifestations

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Cases and figures

  • Case 1: meningeal granulomatosis
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