Alagille syndrome

Case contributed by Dr Jayanth Keshavamurthy


6-year-old male with Alagille syndrome, branch pulmonary artery stenosis and a left pulmonary artery (LPA) stent.

Patient Data

Age: 6
Gender: Male

Stable appearance of the median sternotomy wires with the most inferior wire fractured. Stable pulmonary artery vascular stent. 

No focal areas of consolidation or pleural effusions are identified.

The cardiac silhouette is not enlarged

Case Discussion

Surgery initially, there after multiple cardiac interventions for PA stenosis with stents.

PlayAdd to Share

Case information

rID: 51270
Published: 8th Feb 2017
Last edited: 14th Aug 2019
Inclusion in quiz mode: Included

Updating… Please wait.

 Unable to process the form. Check for errors and try again.

 Thank you for updating your details.